Aggressive fibromatosis - case report

Jelena Roganović, Silvije Šegulja


Aggressive fibromatosis or desmoid tumors are slowly growing fibroblastic neoplasms of intermediate malignancy. They are very rare in children. The optimal treatment modality has not been established. We report a case of a 6-year-old girl with a desmoid tumor of the nasal region. After surgical excision and re-excision, she had an evident local progression and received systemic chemotherapy. The complexity of recognition and multidisciplinary management with an individualized approach is highlighted.


Aggressive fibromatosis; Desmoid tumor; Child

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