Treatment Approach for an Infant with Complex Congenitally Corrected Transposition of the Great Arteries

Abstract

Objective – The aim of the paper is to present a rare and complex congenital heart defect (CHD), congenitally corrected transpo­sition of the great arteries of the heart (ccTGA) with associated anomalies, including ventricular septal defect (VSD), valvular and subvalvular pulmonary stenosis, dysplasia of the tricuspid valve, and atrial septal defect (ASD) with first-degree atrioventricular block, which was diagnosed, monitored and successfully treated with heart surgery in an infant.

Case Report – A female infant was born with 3350 grams in weight, 50 cm in length, oxygen saturation of 98%, and heart rate of 170 beats per minute. The antenatal and perinatal period was normal. CHD was verified by ultrasound at the age of 3 days. Angiotensin-converting-enzyme inhibitors (ACE inhibitors) and diuretics were introduced in therapy after one month. Cardiac surgery (Senning-Rastelli proce­dure with placement of an 18-mm Contegra conduit) was performed at the age of 9 months. After the operation, the infant was stable on therapy with diuretics, antiaggregants, beta blockers, and antianemic therapy with vitamin D in prophylaxis.

 Conclu­sion – ccTGA with associated anomalies is a rare, life-threatening, congenital heart disease. After birth it demands correct diag­nosis, adequate follow-up, and cardiac surgery in infancy